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ITEM PROTEIN ANTIBODY ASSAY KIT CELL
Glycogen Debranching Enzyme (AGL)
Amylo-1,6-Glucosidase,4-Alpha-Glucanotransferase; Glycogen Storage Disease Type III
Debranching enzymes are responsible for transferring three glucose subunits of glycogen from one parallel chain to another. Afterwards, the donator branch will contain only one glucose residue with alpha-1,6 linkage. This remaining residue is in turn cut by alpha-1,6 glucosidase. This two step process is the general process by which the debranching enzymes "straighten out" glycogen into an unbranched glucose polymer.This enzyme has two independent catalytic activities which occur at different sites on the protein: a 4-alpha-glucotransferase activity and a amylo-1,6-glucosidase activity. Mutations in this gene are associated with glycogen storage disease although a wide range of enzymatic and clinical variability occurs which may be due to tissue-specific alternative splicing.
Organism species: Homo sapiens (Human)
CATALOG NO. PRODUCT NAME
Proteins RPD189Hu01 Recombinant Glycogen Debranching Enzyme (AGL) Customize
Antibodies PAD189Hu01 Polyclonal Antibody to Glycogen Debranching Enzyme (AGL) Customize
MAD189Hu21 Monoclonal Antibody to Glycogen Debranching Enzyme (AGL) Customize
Assay Kits SED189Hu ELISA Kit for Glycogen Debranching Enzyme (AGL) Customize
SCD189Hu CLIA Kit for Glycogen Debranching Enzyme (AGL) Customize
Organism species: Mus musculus (Mouse)
CATALOG NO. PRODUCT NAME
Proteins RPD189Mu01 Recombinant Glycogen Debranching Enzyme (AGL) Customize
Antibodies PAD189Mu01 Polyclonal Antibody to Glycogen Debranching Enzyme (AGL) Customize
MAD189Mu21 Monoclonal Antibody to Glycogen Debranching Enzyme (AGL) Customize
Assay Kits SED189Mu ELISA Kit for Glycogen Debranching Enzyme (AGL) Customize
SCD189Mu CLIA Kit for Glycogen Debranching Enzyme (AGL) Customize
Organism species: Rattus norvegicus (Rat)
CATALOG NO. PRODUCT NAME
Proteins RPD189Ra01 Recombinant Glycogen Debranching Enzyme (AGL) Customize
Antibodies PAD189Ra01 Polyclonal Antibody to Glycogen Debranching Enzyme (AGL) Customize
MAD189Ra21 Monoclonal Antibody to Glycogen Debranching Enzyme (AGL) Customize
Assay Kits SED189Ra ELISA Kit for Glycogen Debranching Enzyme (AGL) Customize
SCD189Ra CLIA Kit for Glycogen Debranching Enzyme (AGL) Customize