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ITEM PROTEIN ANTIBODY ASSAY KIT CELL
MpV17 Mitochondrial Inner Membrane Protein (MPV17)
SYM1; Glomerulosclerosis
MPV17 encodes a mitochondrial inner membrane protein that is implicated in the metabolism of reactive oxygen species. Mutations in this gene have been associated with the hepatocerebral form of mitochondrial DNA depletion syndrome (MDDS).The Mpv17 strain of mice carries a transgenically produced retroviral insert in its genome. The integration prevents the expression of the Mpv17 gene, leading to the development of glomerulosclerosis in mice homozygous for the integration. Physiologically and histologically, the phenotype of the kidney disease resembles human glomerulosclerosis. The mice demonstrate nephrotic syndrome at an early age.Sequence analysis demonstrated over 90% identity to the mouse Mpv17 gene in the region coding for a protein of 176 amino acids and unknown function.
Organism species: Homo sapiens (Human)
CATALOG NO. PRODUCT NAME
Proteins RPL752Hu01 Recombinant MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
Antibodies PAL752Hu01 Polyclonal Antibody to MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
MAL752Hu21 Monoclonal Antibody to MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
Assay Kits SEL752Hu ELISA Kit for MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
SCL752Hu CLIA Kit for MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
Organism species: Mus musculus (Mouse)
CATALOG NO. PRODUCT NAME
Proteins RPL752Mu01 Recombinant MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
Antibodies PAL752Mu01 Polyclonal Antibody to MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
MAL752Mu21 Monoclonal Antibody to MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
Assay Kits SEL752Mu ELISA Kit for MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
SCL752Mu CLIA Kit for MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
Organism species: Rattus norvegicus (Rat)
CATALOG NO. PRODUCT NAME
Proteins RPL752Ra01 Recombinant MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
Antibodies PAL752Ra01 Polyclonal Antibody to MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
MAL752Ra21 Monoclonal Antibody to MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
Assay Kits SEL752Ra ELISA Kit for MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize
SCL752Ra CLIA Kit for MpV17 Mitochondrial Inner Membrane Protein (MPV17) Customize