Calpain 3 (CAPN3)
CANPL3; p94; LGMD2; LGMD2A; nCL1; Calcium-activated neutral proteinase 3; Muscle-specific calcium-activated neutral protease 3; New calpain 1
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Calpain, a heterodimer consisting of a large and a small subunit, is a major intracellular protease, although its function has not been well established. CAPN3 encodes a muscle-specific member of the calpain large subunit family that specifically binds to titin.Alternate promoters and alternative splicing result in multiple transcript variants encoding different isoforms and some variants are ubiquitously expressed. In melanocytic cells CAPN3 gene expression may be regulated by MITF.Defects in CAPN3 are the cause of limb-girdle muscular dystrophy type 2A (LGMD2A). LGMD2A is an autosomal recessive degenerative myopathy characterized by progressive symmetrical atrophy and weakness of the proximal limb muscles and elevated serum creatine kinase.
Organism species: Homo sapiens (Human)
- Recombinant protein RPC960Hu01 Recombinant Calpain 3 (CAPN3) In Stock
- Active protein APC960Hu01 Active Calpain 3 (CAPN3) In Stock
- Polyclonal antibody PAC960Hu01 Polyclonal Antibody to Calpain 3 (CAPN3) In Stock
- Monoclonal antibody MAC960Hu22 Monoclonal Antibody to Calpain 3 (CAPN3) In Stock
- Sandwich ELISA SEC960Hu ELISA Kit for Calpain 3 (CAPN3) In Stock
Organism species: Mus musculus (Mouse)
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Organism species: Rattus norvegicus (Rat)
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- Sandwich ELISA SEC960Ra ELISA Kit for Calpain 3 (CAPN3) In Stock
Organism species: Bos taurus; Bovine (Cattle)
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- Sandwich ELISA SEC960Bo ELISA Kit for Calpain 3 (CAPN3) In Stock