Desmoplakin (DSP)
DPI; DPII; KPPS2; PPKS2; DP; 250/210 kDa paraneoplastic pemphigus antigen
Desmosomes are intercellular junctions that tightly link adjacent cells. Desmoplakin is an obligate component of functional desmosomes that anchors intermediate filaments to desmosomal plaques.
The N-terminus of desmoplakin is required for localization to the desmosome and interacts with the N-terminal region of plakophilin 1 and plakoglobin. The C-terminus of desmoplakin binds with intermediate filaments. In the mid-region of desmoplakin, a coiled-coiled rod domain is responsible for homodimerization. Mutations in this gene are the cause of several cardiomyopathies and keratodermas as well as the autoimmune disease paraneoplastic pemphigus.
Organism species: Homo sapiens (Human)
- Recombinant protein RPC203Hu01 Recombinant Desmoplakin (DSP) In Stock
- Polyclonal antibody PAC203Hu01 Polyclonal Antibody to Desmoplakin (DSP) In Stock
- Monoclonal antibody MAC203Hu22 Monoclonal Antibody to Desmoplakin (DSP) In Stock
- Monoclonal antibody MAC203Hu21 Monoclonal Antibody to Desmoplakin (DSP) In Stock
- Sandwich ELISA SEC203Hu ELISA Kit for Desmoplakin (DSP) In Stock
Organism species: Mus musculus (Mouse)
- Customized Service n/a Recombinant Desmoplakin (DSP) Recombinant Protein Customized Service Offer
- Customized Service n/a Monoclonal Antibody to Desmoplakin (DSP) Monoclonal Antibody Customized Service Offer
- Customized Service n/a Polyclonal Antibody to Desmoplakin (DSP) Polyclonal Antibody Customized Service Offer
- Customized Service n/a CLIA Kit for Desmoplakin (DSP) CLIA Kit Customized Service Offer
- Customized Service n/a ELISA Kit for Desmoplakin (DSP) ELISA Kit Customized Service Offer
Organism species: Rattus norvegicus (Rat)
- Customized Service n/a Recombinant Desmoplakin (DSP) Recombinant Protein Customized Service Offer
- Customized Service n/a Monoclonal Antibody to Desmoplakin (DSP) Monoclonal Antibody Customized Service Offer
- Customized Service n/a Polyclonal Antibody to Desmoplakin (DSP) Polyclonal Antibody Customized Service Offer
- Customized Service n/a CLIA Kit for Desmoplakin (DSP) CLIA Kit Customized Service Offer
- Customized Service n/a ELISA Kit for Desmoplakin (DSP) ELISA Kit Customized Service Offer