Loricrin (LOR)
Loricrin is a major protein component of the cornified cell envelope found in terminally differentiated epidermal cells. Mutations in this gene are associated with Vohwinkel's syndrome and progressive symmetric erythrokeratoderma, both inherited skin diseases.
There were multiple sequence variants within these 2 size class alleles due to various deletions of 12 bp (4 amino acids) in the major loop of this glycine loop domain. By use of a specific loricrin antibody in immunogold electron microscopy, they showed that loricrin appears initially in the granular layer of human epidermis and forms composite keratohyalin granules with profilaggrin, but localizes to the cell periphery (cell envelope) of fully differentiated stratum corneum cells.
Organism species: Homo sapiens (Human)
- Recombinant protein RPC568Hu01 Recombinant Loricrin (LOR) In Stock
- Recombinant protein RPC568Hu02 Recombinant Loricrin (LOR) In Stock
- Polyclonal antibody PAC568Hu01 Polyclonal Antibody to Loricrin (LOR) In Stock
- Monoclonal antibody MAC568Hu22 Monoclonal Antibody to Loricrin (LOR) In Stock
- Polyclonal antibody PAC568Hu02 Polyclonal Antibody to Loricrin (LOR) In Stock
- Sandwich ELISA SEC568Hu ELISA Kit for Loricrin (LOR) In Stock
Organism species: Mus musculus (Mouse)
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- Sandwich ELISA SEC568Mu ELISA Kit for Loricrin (LOR) In Stock
Organism species: Rattus norvegicus (Rat)
- Customized Service n/a Recombinant Loricrin (LOR) Recombinant Protein Customized Service Offer
- Customized Service n/a Monoclonal Antibody to Loricrin (LOR) Monoclonal Antibody Customized Service Offer
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