Retinaldehyde Binding Protein 1 (RLBP1)
CRALBP; Cellular retinaldehyde-binding protein
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Retinaldehyde-binding protein 1 is a 36-kD water-soluble protein which carries 11-cis-retinaldehyde or 11-cis-retinal as physiologic ligands. It may be a functional component of the visual cycle. Mutations of this gene have been associated with severe rod-cone dystrophy, Bothnia dystrophy (nonsyndromic autosomal recessive retinitis pigmentosa) and retinitis punctata albescens. CRALBP is not expressed in photoreceptors but is abundant in the retinal pigment epithelium (RPE) and Muller cells of the neuroretina, where it carries 11-cis-retinol and 11-cis-retinaldehyde. When expressed in bacteria, recombinant CRALBP containing the R150Q substitution was less soluble than wildtype recombinant CRALBP. Mutant CRALBP was purified and found to lack the ability to bind 11-cis-retinaldehyde.
Organism species: Homo sapiens (Human)
- Recombinant protein RPC776Hu01 Recombinant Retinaldehyde Binding Protein 1 (RLBP1) In Stock
- Polyclonal antibody PAC776Hu01 Polyclonal Antibody to Retinaldehyde Binding Protein 1 (RLBP1) In Stock
- Monoclonal antibody MAC776Hu21 Monoclonal Antibody to Retinaldehyde Binding Protein 1 (RLBP1) In Stock
- Sandwich ELISA SEC776Hu ELISA Kit for Retinaldehyde Binding Protein 1 (RLBP1) In Stock
Organism species: Mus musculus (Mouse)
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- Customized Service n/a Polyclonal Antibody to Retinaldehyde Binding Protein 1 (RLBP1) Polyclonal Antibody Customized Service Offer
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Organism species: Rattus norvegicus (Rat)
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- Customized Service n/a Monoclonal Antibody to Retinaldehyde Binding Protein 1 (RLBP1) Monoclonal Antibody Customized Service Offer
- Customized Service n/a Polyclonal Antibody to Retinaldehyde Binding Protein 1 (RLBP1) Polyclonal Antibody Customized Service Offer
- Customized Service n/a CLIA Kit for Retinaldehyde Binding Protein 1 (RLBP1) CLIA Kit Customized Service Offer
- Customized Service n/a ELISA Kit for Retinaldehyde Binding Protein 1 (RLBP1) ELISA Kit Customized Service Offer