Troponin T Type 1, Slow Skeletal (TNNT1)
ANM; STNT; TNT; TNTS; Slow Skeletal Muscle Troponin T
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TNNT1 is a regulatory complex located on the thin filament of the sarcomere. This complex regulates striated muscle contraction in response to fluctuations in intracellular calcium concentration. This complex is composed of three subunits: troponin C, which binds calcium, troponin T, which binds tropomyosin, and troponin I, which is an inhibitory subunit. This protein is the slow skeletal troponin T subunit. Mutations in this gene cause nemaline myopathy type 5, also known as Amish nemaline myopathy, a neuromuscular disorder characterized by muscle weakness and rod-shaped, or nemaline, inclusions in skeletal muscle fibers which affects infants, resulting in death due to respiratory insufficiency, usually in the second year. Multiple transcript variants encoding different isoforms have been found for this gene.
Organism species: Homo sapiens (Human)
- Recombinant protein RPD231Hu01 Recombinant Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Active protein APD231Hu01 Active Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Polyclonal antibody PAD231Hu01 Polyclonal Antibody to Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Labelled antibody LAD231Hu71 Biotin-Linked Polyclonal Antibody to Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Labelled antibody LAD231Hu81 FITC-Linked Polyclonal Antibody to Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Monoclonal antibody MAD231Hu21 Monoclonal Antibody to Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Sandwich ELISA SED231Hu ELISA Kit for Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
Organism species: Mus musculus (Mouse)
- Recombinant protein RPD231Mu01 Recombinant Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Recombinant protein RPD231Mu02 Recombinant Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Polyclonal antibody PAD231Mu01 Polyclonal Antibody to Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Polyclonal antibody PAD231Mu02 Polyclonal Antibody to Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Sandwich ELISA SED231Mu ELISA Kit for Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
Organism species: Rattus norvegicus (Rat)
- Recombinant protein RPD231Ra01 Recombinant Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Polyclonal antibody PAD231Ra01 Polyclonal Antibody to Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Monoclonal antibody MAD231Ra21 Monoclonal Antibody to Troponin T Type 1, Slow Skeletal (TNNT1) In Stock
- Sandwich ELISA SED231Ra ELISA Kit for Troponin T Type 1, Slow Skeletal (TNNT1) In Stock